Behçet’s disease in a 15 years old boy: case report

1 Klinika Chorób Płuc i Reumatologii Dziecięcej, Uniwersytet Medyczny w Lublinie.
Kierownik Kliniki: prof. dr hab. n. med. Ewa Tuszkiewicz-Misztal
2 Klinika Onkohematologii Dziecięcej, Uniwersytet Medyczny w Lublinie. Kierownik Kliniki: prof. dr hab. n. med. Jerzy Kowalczyk
Correspondence to: dr n. med. Jacek Postępski, Klinika Chorób Płuc i Reumatologii Dziecięcej Uniwersytetu Medycznego
w Lublinie, Dziecięcy Szpital Kliniczny, ul. W. Chodźki 2, 20-093 Lublin, tel.: 81 718 54 50, e-mail: jacek.postepski@op.pl
Source of financing: Department own sources

Pediatr Med rodz Vol 5 Numer 4, p. 291-295
ABSTRACT

Behçet’s disease (BD), usually occurring in eastern Asia, the Middle East and eastern Mediterranean, is rarely reported in children in Central and Northern Europe. The disease can be diagnosed on the basis of certain symptoms according to international criteria, when other explanations are not available or convincing. BD is characterized by a triad of recurrent aphthous stomatitis, genital ulceration, skin and eye lesions. The aetiology is unknown, but systemic vasculitis is the main pathology. Case report: A 15 years old male was found to suffer from recurrent oral and scrotal ulcerations and episodes of acute epididymitis of unknown origin. In the course of the disease, an episode of erythema nodosum was also noted. On ophthalmologic examination, hypopyon and acute uveitis were reported. The patient fulfilled the criteria for BD (Criteria of the International Study Group for the Diagnosis of Behçet’s Disease, 1990). Although the clinical course of the disease was typical for BD, the diagnosis was formulated only after about 12 months. Conclusions: BD is incidentally reported in children in Central Europe although this type of vasculitis plays an important role in the differential diagnosis in patients with recurrent oral and genital ulcerations.

Keywords: Behçet’s disease, children, systemic vasculitis, diagnostic criteria, clinical signs